Pakati pezvirwere zvakawanda zvinokonzerwa nejen mutation, cystic fibrosis yemapapu iri pamusoro pezvinyorwa. Izvi zvirwere zvinosanganiswa nekuputsika kwehutano hwechakavanzika chakavanzwa nhengo dzomukati, izvo zvinotungamirira mukukundwa kwehutano hwemapfupa uye chirwere chepamuviri.
Genetic disease ye cystic fibrosis
Chirwere chiri mubvunzo chinonziwo cystic fibrosis. Iyo inoratidzwa nehupamhi hwepamusoro uye ine simba yakasvikidzika yemascus, iyo inofukidza nhengo dzisina kumira. Somugumisiro wechirongwa ichi, kuvharidzira kunowedzera, uye mabhakitiriya anonzi pathogenic anoita kuti kuvhiringidza kuwedzere kuwedzera.
Cystic fibrosis yemapapu ine chikonzero chimwe chete - kukuvadza kwechinomwe chromosome (refu yakareba). Maererano nehuwandu, mutakuri wechirwere ichi munhu wese wemakumi maviri ari panyika. Mikana yechirwere ndeye 25%, kunze kwekuti vabereki vose vane chirwere chakakanganiswa.
Kune marudzi matatu echirwere ichi:
- intestinal cystic fibrosis;
- pulmonary kana kupumha cystic fibrosis;
- yakasiyana-siyana (pulmonary cystic fibrosis).
Cystic fibrosis yemapapu - zviratidzo
Zviratidzo zvikuru zvechirwere ichi:
- kunyunyisa kwevakisiki, mazamu akaoma panguva yekukanganiswa;
- kuwedzera kunowedzera kwepineumonia, bronchitis, pneumonia;
- kukanganiswa kwemukati;
- dehydration;
- kurwadziwa, kusagadzikana mudumbu;
- kuwedzera chido chekudya nehuwandu husina kukwana uye kukura mumuviri;
- matambudziko epabonde;
- pancreatitis ;
- kuwedzera kweminwe pamaoko;
- chiropa chiropa;
- chirwere cheshuga mellitus;
- sinusitis ;
- kuputsika kwemapfupa;
- kupera kwemukati (kurudyi).
Iyo yemapurmonary ye cystic fibrosis inozviratidza mumakore maviri okutanga ehupenyu, inoratidzwa nehuwandu hwekuvhara mukati pakati nepaduku yebronchi yemwana.
Cystic Fibrosis - Kuziva uye Kuongorora
Kuongororwa kunoitwa nemitemo mina yepamusoro.
Chokutanga pane zvose, kuvapo kweiyo yakakanganiswa muvabereki uye nenyaya dzezviitiko mumhuri dzinoongororwa. Migumisiro inobatsira, pamwe nekuonekwa kwechirwere chisingaperi chemapapu mumapapu uye bronchi, kuvapo kwepamuviri chirwere, kunopa nzvimbo yekuita jira test. Iyo inosanganisira kugadzirisa huwandu hwemaswa mumvura inosunungurwa ne pores. Kuti aite iyo nzira, nzvimbo shomanana paruoko (pamusoro pemheto) inobatwa nechirwere chinonzi pilocarpine. I electrode inowanikwa munzvimbo ino, inokonzera kusunungurwa kwekutuka, iyo iri kurega nemapulazi epurasitiki kana kuti kupisa-kupisa, zvichigadzira mamiriro e-sauna. Mushure memaminitsi makumi mana, iyo yakabudiswa mvura inoiswa munyu kuongorora. Kana huwandu hwayo hwakapfuura mitezo yakasimbiswa, kugadziriswa kwekupedzisira kunoitwa.
Cystic fibrosis yemapapu - kurapwa
Chimiro chechirwere hachibvumi kuti chirape zvachose, chirwere chinotarisirwa kugadzirisa zviratidzo uye zvinoda nzira yakabatana. Mishonga inosanganisira mabasa anotevera:
- kwenguva refu yemishonga inorwisa mabhakitiriya;
- mukana wokugamuchira mucolytics;
- kinesitherapy;
- Inhalation ye corticosteroid hormone uye beta mimetics;
- kushandisa bronchodilator;
- achiita kuporesa maitiro;
- kururamiswa kwezvokudya pamwe nekuwedzera kwekubhadhara kwezuva nezuva ne 10-15%;
- autogenous lung drainage;
- bug-massage;
- kugamuchirwa kwevhithamini uye microelements.
Yakanyanya uye inobudirira chaizvo panguva iyo nzira yekurapa isapfu transplantation. Mukuwedzera, tsvakurudzo yezvechiremba inogara ichiitwa kuitira kugadzirisa jena rakakanganisika kuburikidza nehutachiona hunogadzirwa.