Cystic Fibrosis - Zviratidzo

Sezvo mutemo, zvinoita kuti uongorore cystic fibrosis achiri muduku, sezvo inoratidzwa nechiratidzo chechimiro chakanyanya. Asi muchimiro chinyoro kana chinononoka chichirudzika, chirwere ichi chinoratidzika chisina kunaka. Saka zvakakosha kuziva, kuitira kusiyanisa kubva kune dzimwe zvirwere zvakafanana zvakananga cystic fibrosis - zviratidzo uye zviratidzo zvekunze.

Denda re cystic fibrosis - chii ichocho?

Chirwere chiri mubvunzo, pane kudaro, chirwere. Iko kunokonzerwa nekuchinja kwegene inowanikwa munzvimbo yakareba yechishanu ye chromosome. Mikana yekurwara ndeye chete kana vabereki vose vari kutakura gero rakaparadzwa, uye ndeye 25%. Pasinei nemamiriro ezvinhu aya, chirwere che cystic fibrosis chinokanganisa nhamba yakakwana yevanhu, sezvo chromosome ine mutende iripo kune vose vane makumi maviri vanogara panyika.

Cystic Fibrosis muVakuru - Zviratidzo

Sezvinenge zvataurwa, chirwere chinozviratidza muhuduku, kazhinji kusvika pamakore maviri, uye chete 10% yevarwere vane zviratidzo zvokutanga zvinowanikwa mukuyaruka uye munhu mukuru.

Zviratidzo zvikuru zve cystic fibrosis ndezvi:

Zviratidzo zvakarongwa zve cystic fibrosis zvakabatana nekuti gira rakakanganiswa haibvumiri muviri kuti uite puroteni iyo inokonzera chirwere chemvura-electrolyte metabolism muzvikamu zvemuviri. Izvi zvinokonzera kuwedzera kwehuwandu hwevanhu uye hutachiona hwehutachiona hwakagadzirwa nemafungiro akawanda emukatikati mukati. Mucus inoputika, mabhakitiriya anowedzera mauri, uye kuchinja kusingagadziki kunowanikwa munhengo, zvikuru mumapapu.

Nzira yemukumbo ye cystic fibrosis inozivikanwa nokudzima, kubata, kuvhiringidza uye kurutsa. Zviratidzo izvi zvinokodzera kurapwa nekutora mishonga nemakemikari, asi zviratidzo zvezvirwere zvechirwere zvinoramba zvichiwedzera.

Cystic Fibrosis - Kuziva

Chokutanga, kuvapo kwezviratidzo zvinoratidza kuti chirwere chacho chinongororwa-chekuvhenekera kwechakavanzika chemuviri mutsva, kuwedzera kwezvirwere zvisingaperi zvekufema. Mushure meizvi, zvakakosha kusimbisa kuvepo kwechibereko chekutengesa kubva kuvabereki uye kutarisa matambudziko ekuderedza mumhuri.

Kunyatsoongorora kwakakwana kwe cystic fibrosis DNA. Uyu muedzo ndiyo inonyanya kunzwisisika, uye inogona kuitwa kunyange panguva yekusununguka nekuongorora amniotic fluid. Nhamba yemigumisiro yemanyepo haina kudarika 3% uye inokubvumira kuti uone nekukurumidza pasina zviyero zvakare.

Kusarudza kuwanda kwemafuta acids uye chymotrypsin mumubhedha wemurwere ndeimwe nzira yekuongorora chirwere chacho. Nhamba dzemazuva ano dzomu chymotrypsin dzinogadzirwa mumwe nomumwe mubato re laboratory. Nhamba yeacids inokonzera kukanganisa kwe cystic fibrosis inopfuura 20-25 mmol pazuva.

A sweat test for cystic fibrosis ne pilocarpine ndeyekudzidza kwemajiramu emakloride mumvura yakachengetwa ne pores. Muedzo unofanirwa kuongororwa kanenge katatu kuti ugadzirise kunyatsoongorora.