Vana-Makunguti ... Kwekutanga kokunzwa mazwi aya, vakawanda vanobva vafungidzira mafungu anovaraidza, asinganyatsogoni kuputika pakati pemaruva uye kufara kwehucheche, vasingachagadziriswi nekuora mwoyo uye kushungurudzika. Munguva iyi, hupenyu hwevana vane butterfly syndrome haimbofanani nenyaya yemafano kana kuti mifananidzo yakanaka. Muchikamu chino tichataura nezve congenital bullous epidermolysis - chirwere chisina kujairika chinokanganisa ganda remuviri womunhu.
Bullous Epidermolysis: Zvinokonzera
Sezvo mutemo, vabereki vevana vafurakiti vanodzidza nezvehutano hweganda remwana wavo mumazuva okutanga (uye kunyange maawa) mushure mokuberekwa kwechecheche. Kwenguva yokutanga chirwere ichi chakatsanangurwa sekupera kwemakore ekuma1900, muna 1886.
Chinokonzera chirwere ichi ndicho chiremera chemajini chinoshaya chirwere chepidermal yekwanisi yekuita basa rinodzivirirwa. Ichi chakaremara chinoparadzirwa kubva kuvabereki vanovhiringidza, kana kuti vanobuda pakarepo. Somugumisiro, ganda rose (kusanganisira mucous membrane) rinova rakaoma zvikuru - kusanganisa kuduku kunogona kukonzera kukanganisa. Kana zvisina kudaro, vana vakadaro vakakwana zvakakwana-havaregi mushure mekusimudzira pfungwa uye mupfungwa, vanokura kazhinji uye nerubatsiro rwavanogona kuva chikamu chakazara chevanhu.
Maitiro ehaka yechirwere ichi haasati aonekwa - varwere vane nzara epidermolysis vanogona kuva nehutano uye vana vanorwara. humwe hutano hwechirwere ndechokuti asati aberekwa mwana hazvibviri kuzviongorora nemhando ipi zvayo inoratidzika yezvokurapa - uye iyo ultrasound ye fetus kana kuongorora kwebhroreta inobereka migumisiro.
Nguva yakakosha yehupenyu yeveveredzi vana kune makore matatu. Mune ramangwana, nekurapa kwakanaka uye kutarisirwa, ganda rinowedzera zvishoma, rinowedzera kugadzikana, kunyange risingapindi simba reganda remuviri wevanhu. Mukuwedzera, vana vaduku havakwanisi kuziva nezvechikonzero-kubudirira kwehukama, havagoni kutsanangura kuti hazvigoneki, somuenzaniso, kutamba pamabvi avo, sezvo ganda remakumbo mushure mezvo rakanyatsopera "kubvisa", kana kusvina maziso kana matama.
Bullous epidermolysis: kurapwa
Mhedzisiro yeveveredzi vana yakaoma, nokuti chirwere chinokonzera kutambura kwakanyanya hachiregi nhasi. Zvose zvinogona kuitirwa vana vakadaro ndezvekuedza kuchengetedza ganda ravo risina kusimba kubva pakakuvadzwa (izvo zvakaoma kwazvo), uye kana zviitiko zvavo zvichiitika zvakanaka uye panguva yakakodzera kuzvitarisira. Asi pasinei neizvi, munyika dzakawanda dzakagadziriswa zvirongwa zvekutarisira varwere uye mapoka ehutano hwehupenyu hwose hwakagadzirwa, izvo zvinovabvumira kutungamirira hupenyu hune hupenyu, kugamuchira dzidzo, kutungamirira hupenyu hwehupenyu hwehupenyu uye kunyange kutamba mitambo.
Mune CIS, nechinorwara chebondous epidermolysis, kufungidzira kunowanzosakanganisika, nokuti chirwere chacho hachiwanzoitiki, vanachiremba havana chavanoziva pakurapa varwere vakadaro, uye mune dzimwe nguva kunyange vasingatombofungi kuti kune chirwere ichi. Kazhinji vabereki vanowedzera mamiriro ezvinhu, vachizvipa mishonga uye vachiedza kurapa kukanganisa kweganda recheche rinonzi phytotherapeutic, mavara anozvigadzira uye vatauriri, bluehead nemamwe nzira dzorudzi urwu. Hazvina maturo kutaura, mushure mekunge "kurapwa" kwakadaro, mari yekudzorera epidermis yemwana inowedzera kusvika kumasikirwo emasikirwo, asi kunyatsokwana panguva yakakodzera kunotonyanya kuoma, asi zvisingadhuri. Butterfly vana vanoda
Nokuda kwekusaziva kurapa kwehutano uye zvehutano, kusakwanisa ruzivo pakuchengetedza uye kurapwa, vana vakawanda vane bullous epidermolysis vanofa vachiri vaduku.
Ichokwadi kuti kuchengetwa kweganda uye mararamiro evana vafurakiti zvakasiyana zvakanyanya zvichienderana nekuoma kwechirwere - chiremera chimiro uye zvakanyanya kufananidzira zviratidzo, kunyatsotarisa uye kwakarurama kutarisira uye kurapwa kwomwana kunofanira kuva.