Chirwere cheBehcet

Chirwere cheBehcet chirwere chisingaperi chisingadzokizve, chirwere chinowanzoonekwa muJapan uye kuMediterranean. Kazhinji kazhinji inowedzera kune vanhu vane makore makumi matatu nemakore makumi mana. Ichi chirwere ndechechikwata chevasculitis uye ine etiology isina kufanirwa.

Zvinokonzera Matwere aBeccet

Kubudirira kwechirwere kunobatanidza nezviverengero zvinotarisa, izvo zvinotevera ndezvipi:

Nyanzvi dzakawanda dzinofunga kuti kutanga kwechirwere cheBeççet kunokonzerwa nezvinhu zvinotapukira, uye mune ramangwana, maitiro ezvigadziro anowanikwa kwavari, zvichienderana nekugara nhaka.

Zviratidzo zvehosha yeBehcet muvakadzi

Ichi chirwere chinoratidzirwa nehuwandu. Muchiitiko ichi, zviratidzo zvikuru, izvo zvingaita kuti iwe uone zvakajeka, zvinobatanidzwa nekukuvadza kune mucous membrane yemuromo nemaronda, pamwe chete nekuputira maitiro mumaziso. Funga zvose zviratidzo zvechirwere cheBehçet mune zvakawanda.

Chirevo chemuviri chinokanganisa

Pakutanga, zviduku zviduku zvine zvinyorwa zvinowanikwa mumiromo, denga, rurimi, gums, pharynx, mukati mematama, izvo zvinozozarurwa. Panzvimbo yeva vesicles, zvakakomba, maronda anorwadza (aphthae) emucheka wakajeka wakaumbwa akaumbwa, iyo yakakura iyo inogona kusvika 2 cm muupamhi. Kuporeswa kwezvironda kunowanikwa mushure memwedzi gare gare, ne 3-4 nguva gore gore rinosuruvara.

Zvirwere zvechirwere

Vakadzi vari mumuchembera yemakadzi uye vhuvha vanoita maronda, kazhinji anorwadza, akafanana neaya anoonekwa mumuromo. Mushure mokuporeswa, zviyo zvinogona kugara munzvimbo yavo.

Kushungurudzika kwemaonero

Izvi zviratidzo zvinouya mavhiki mashoma mushure mezviratidzo zviri mumuromo. Varwere vanogona kukura nekuputika kwe iris uye ciliary muviri weziso reziso, kuputika kwevascular uye mucous membranes yeziso, kupisa kwekonoa. Kakawanda pane zviratidzo zvinotevera: photophobia, maonero asina kunaka, kuwedzera kukutuka.

Zviratidzo zvakajeka

Nodhema yemaily, pyoderma, mapulo-vesicular rash inogona kuonekwa. Uyewo pane dzimwe nguva, matendere anorema bvudzi, subungual panaritium inoonekwa.

Matambudziko e musculoskeletal system

Ikoko kune kukura kweArthritis (kazhinji pfupi pamagumo) pasina zvinoparadza zvinhu.

Neurological zviratidzo

Pane zviratidzo zvekunyangarika kwehutano hwehutano, kukura kwe meningoencephalitis, edema ye optic nerve disk, kuonekwa kwehemiparesis.

Intravascular inflammatory changes

Unhu hwekuvandudzwa kwevasculitis, thrombophlebitis yemaketani pamakumbo, thrombosis yemaketani ehepatic uye thromboembolism yemapurmonary arteri, aneorysm aortic, nezvimwewo.

Nezvipembenene zvemuviri wepamuviri, moyo nemapapu, zvinogona kuva nezviratidzo zvakadaro:

Kurapa kwezvirwere zveBehcet

Kurapa kwechirwere cheBehcet, kutanga kwezvose, chinangwa chekuwedzera hupenyu hwevarwere, kubudirira kwekuregererwa kwenguva refu uye kudzivirira kuchinja kusingagadziriswi munhengo dzomukati.

Zviratidzo zveBehcet's syndrome zviri mumuromo wemumuromo uye pamakumbo edzimba zvinotarisirwa nehutano hwemunharaunda nekushandiswa kweglucocorticosteroids , antiseptic solutions, uye dzimwe nguva - antipodal agents. Uyewo pakurapa kwechirwere, cytostatic agents, immunosuppressors, mavitamini anogona kurongerwa. Utachiona hwevascular hunobatwa nemaitiro ekuvhiya. Varwere vazhinji vanorayirwa extracorporal hemocorrection. Kurapa kunoitwa pasi pekutariswa kwechiremba nguva dzose.