Lyell's Syndrome

Lyell's syndrome (zita rechipiri ndiStevens-Johnson syndrome) inonyanya kurwisa, inoratidzwa muuto uye rufu rwepamusoro peganda, pamwe nekudhakwa kwechimiro chose nemhaka yehupenyu hunoramba huchiitika. Lyell's syndrome inonzi ndiyo yechipiri yakaoma zvikuru shure kwevanaphylactic kushungurudzwa pamusana pemamiriro anobva ku hypersensitivity yemunhu kune zvimwe zvinhu. Lyell's syndrome, inonzi "inouraya epidermal necrolysis", yakatanga kurondedzerwa muna 1956, asi kusvika ikozvino hapana kubvumirana munharaunda yezvokurapa pamusoro pekutanga kwechirwere.


Zvinokonzera Lyell's Syndrome

Kakawanda, chirwere cheRyell chinomuka sechinhu chisingaiti:

Mune zvimwe zviitiko hazvibviri kugadzirisa zvikonzero zvinokonzerwa neIdiopathic reaction, asi, sezvinonzi nyanzvi dzinoti, boka rekutengesa rinosanganisira vanhu vanotambura:

Zviratidzo zveRyell's Syndrome

Chirwere ichi chinowanzotanga nekukwira kwekuwedzera kwe 40 degrees kana kupfuura. Muchiitiko ichi, murwere ane chirwere chakanyanya uye kurwadziwa kweziso. Kuoma uye kubuda kwemahara kunoonekwa. Mushure mechinguva, kuputika kunowanikwa paganda, kufanana nemashes mu measles uye scarlet fever, pamwe chete nekuchenesa kana kunzwa kunorwadza. Kutanga, nzvimbo dzakasvibiswa dzakasvibiswa dzinowanikwa munzvimbo inoputika uye munzvimbo dzemajoka e-axillary, zvino zvishoma nezvishoma vanotanga kutora nzvimbo yose yemuviri.

Chimwe chinhu chinonzi Lyell's syndrome ndicho chikwata cheganda epidermis uye kunyange kunyanya kushamwaridzana neganda remurwere. Izvi zvinovhura kubuda ropa kunokonzera. Mune dzimwe nzvimbo yeheteti, mabhubu anoumbwa, ayo, kana akazarurirwa, anoratidza nzvimbo huru dzakasvibira nes serous exudate. Utachiona hwechipiri hunofamba hunokonzera kukonzera kusunungurwa, kunokonzera kunhuhwirira kwakashata kubva mumuviri. Mucous membrane yemuromo, maziso uye zviito zvemuviri zvinowanikwawo kuchinja kusina kunaka. Dambudziko guru kune utano uye hupenyu hunomiririrwa ne:

Kurapa kweLyell's Syndrome

Kana pane zviratidzo zvehutachiona, iwe unofanirwa kudana ambulensi. Murwere anogadzirirwa muchikwata chikuru chekuchengetedza kana chikwata chikuru chekuchengetedza. Mamiriro ekugara panguva imwechete akafanana neaya anogadzirwa kune varwere vane kupisa uye frostbite. Icho chinodiwa chikuru chekutarisirwa uye kurapwa hazvina maturo. Sangano rerapi muRyell syndrome rinotevera:

  1. Kubviswa kwemishonga yose yakashandiswa kusati kwatanga kufambiswa kwechirwere.
  2. Glucocorticosteroids inorayirwa.
  3. Kurongeka kwehutano kunoshandiswa nemafuta emiriwo uye vitamini A.
  4. Saline uye colloidal solutions zvinokurudzirwa kuti zvizadzire mvura yakasakara nemuviri.
  5. Immunomodulators anoshandiswa.
  6. Kana uchisangana nechirwere chechipiri, antiseptics uye antibiotics zvinoshandiswa.

Nenguva yakakodzera uye yakarurama yakarapwa inobatsira nokukurumidza kusvika pakuwana murwere ane Lyell's syndrome.